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An Official Publication of the Indian Association of Oral and Maxillofacial Pathologists


 
CASE REPORT Table of Contents   
Year : 2014  |  Volume : 18  |  Issue : 4  |  Page : 131-134
Dentinogenesis imperfecta type I: A case report with literature review on nomenclature system


1 Departments of Oral Medicine and Radiodiagnosis, Krishnadevaraya College of Dental Sciences and Hospital, Bangalore, Karnataka, India
2 MS Ramaiah Dental College and Hospital, Bangalore, Karnataka, India

Correspondence Address:
D Devaraju
Department of Oral Medicine and Radiodiagnosis, Krishnadevaraya College of Dental Sciences and Hospital, Hunasamaranahalli, Yelahanka, International Airport Road, Bangalore - 562 157, Karnataka
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/0973-029X.141363

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Dentinogenesis imperfecta (DI) is an inherited disorder affecting dentin. Defective dentin formation results in discolored teeth that are prone to attrition and fracture. Mutation in dentin sialophosphoprotein (DSPP) has been found to cause the dentin disorders DI - I and II (shields II and III). Early diagnosis and treatment of DI is recommended as it may prevent or intercept deterioration of the teeth and occlusion and improve esthetics. Here, we report a case with characteristic clinical, radiological and histological features of DI-I. The etiology and classification followed in literature is confusing since dentinoenamel junction (DEJ) in DI seems to be structurally and functionally normal and DI is clearly a disorder distinct from osteogenesis imperfecta (OI), but we still relate etiology of DI to DEJ and follow Shields classification. Therefore, we have briefly reviewed etiology and nomenclature system of DI.


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Journal of Oral and Maxillofacial Pathology | Published by Wolters Kluwer - Medknow
Online since 15th Aug, 2007