Home About us Editorial board Ahead of print Current issue Search Archives Submit article Instructions Subscribe Contact Us Login 
An Official Publication of the Indian Association of Oral and Maxillofacial Pathologists


 
CASE REPORT - MISCELLANEOUS Table of Contents   
Year : 2019  |  Volume : 23  |  Issue : 4  |  Page : 126-129
Association of enamel-renal syndrome with sialolith: A rare entity


1 Department of Oral and Maxillofacial Surgery, Mahe Institute of Dental Sciences and Hospital, Puducherry, India
2 Department of Oral Medicine, King Khalid University College of Dentistry, Abha, Kingdom of Saudi Arabia
3 Department of Oral Pathology and Microbiology, Mahe Institute of Dental Sciences and Hospital, Puducherry, India
4 Department of Orthodontics, Mahe Institute of Dental Sciences and Hospital, Puducherry, India

Correspondence Address:
Manickam Selvamani
Department of Oral Pathology and Microbiology, Mahe Institute of Dental Sciences, Mahe, Puducherry
India
Login to access the Email id

Source of Support: None, Conflict of Interest: None


DOI: 10.4103/jomfp.JOMFP_9_18

Rights and Permissions

Amelogenesis imperfecta (AI) is a disease primarily affecting amelogenesis, but other various aberrations have been reported in association with this entity. Enamel-renal syndrome (ERS) is a very rare disorder associating AI with nephrocalcinosis. It is known by various synonyms such as AI nephrocalcinosis syndrome, MacGibbon syndrome, Lubinsky syndrome and Lubinsky–MacGibbon syndrome. The purposes of this article are to describe other dental anomalies which are rarely associated with AI making the diagnosis of AI a complex disorder and also to report a rare case of MacGibbon syndrome presented with sialolith of submandibular gland duct which is the first reported case in the literature.


[FULL TEXT] [PDF]*
Print this article  Email this article
    

  Similar in PUBMED
    Search Pubmed for
    Search in Google Scholar for
  Related articles
   Citation Manager
  Access Statistics
   Reader Comments
   Email Alert *
   Add to My List *
 * Requires registration (Free)
 

 Article Access Statistics
    Viewed42    
    Printed2    
    Emailed0    
    PDF Downloaded11    
    Comments [Add]    

Recommend this journal

 

Journal of Oral and Maxillofacial Pathology | Published by Wolters Kluwer - Medknow
Online since 15th Aug, 2007